Shone's Syndrome

Shone’s syndrome also called as Shone’s complex or Shone’s anomaly, is a rare congenital heart disease described by Shone in 1963. It mainly comprises of a set of four left sided cardiac defects namely supravalvular mitral membrane (SVMM), parachute mitral valve, subaortic stenosis (membranous or muscular) and coarctation of the aorta. Out of these four defects, supravalvular mitral membrane (SVMM) is the first to occur which then causes the development of other three defects. It is an obstruction caused to the inflow and outflow of the left ventricle. So, the prognosis depends on the degree of obstruction that is being caused to the flow of blood.