• strict warning: Non-static method view::load() should not be called statically in /home/hc/public_html/sites/all/modules/views/views.module on line 906.
  • strict warning: Declaration of views_handler_filter::options_validate() should be compatible with views_handler::options_validate($form, &$form_state) in /home/hc/public_html/sites/all/modules/views/handlers/views_handler_filter.inc on line 607.
  • strict warning: Declaration of views_handler_filter::options_submit() should be compatible with views_handler::options_submit($form, &$form_state) in /home/hc/public_html/sites/all/modules/views/handlers/views_handler_filter.inc on line 607.
  • strict warning: Declaration of views_handler_filter_boolean_operator::value_validate() should be compatible with views_handler_filter::value_validate($form, &$form_state) in /home/hc/public_html/sites/all/modules/views/handlers/views_handler_filter_boolean_operator.inc on line 159.
  • strict warning: Declaration of views_plugin_style_default::options() should be compatible with views_object::options() in /home/hc/public_html/sites/all/modules/views/plugins/views_plugin_style_default.inc on line 24.
  • strict warning: Declaration of views_plugin_row::options_validate() should be compatible with views_plugin::options_validate(&$form, &$form_state) in /home/hc/public_html/sites/all/modules/views/plugins/views_plugin_row.inc on line 134.
  • strict warning: Declaration of views_plugin_row::options_submit() should be compatible with views_plugin::options_submit(&$form, &$form_state) in /home/hc/public_html/sites/all/modules/views/plugins/views_plugin_row.inc on line 134.
  • strict warning: Non-static method view::load() should not be called statically in /home/hc/public_html/sites/all/modules/views/views.module on line 906.

What is Hypoplastic Right Heart Syndrome and How Much is its Life Expectancy?

26 Jun 2011
Posted by sansadds

The Hypoplastic right heart syndrome (HRHS) is rare congenital disorder. Hypoplasia means underdevelopment of an organ. Thus Hypoplastic right heart syndrome is underdevelopment or incomplete development of the right side of the heart. The structures of the right side of the heart, which includes the right atrium, right ventricles, pulmonary valve, and pulmonary artery, are poorly developed. As a result, the functions of the right sides of the heart are hampered leading to a series of symptoms described as a syndrome. Since the ventricles fails to grow, the right ventricular muscles are also not developed and cannot pump the blood efficiently into the lungs. Thus it results in diminished oxygenation and the baby becomes cyanosed or blue. 

HRHS needs to be treated immediately as the heart fails immediately after birth. The baby shows difficulty in breathing, and the skin, nails, lips and the rest of the body turns blue. Though highly fatal, corrective surgery can rescue the baby for an improved life expectancy. Open heart surgeries, Norwood operation and cardiac transplantation are the treatment options usually considered. After the Fontan (Norwood) procedure, patients have lived a normal life for up to 15 to 30 years, after which the heart functions may show deterioration. Today most parents choose heart transplant for longer and healthier life. 
Children with HRHS should be restricted from heavy activities and sports that could easily exhaust them. Besides a regular cardiac assessment and check up is important. 
Tags: